Noboru Morikawa, Satoshi Mikami, Daisuke Suzuki
A 65-year-old woman with primary Sjögren's syndrome without a history of immunosuppressive therapy presented with progressively enlarging pulmonary nodules showing calcification and cystic changes, mimicking malignancy. Histological examination confirmed AL λ-type nodular pulmonary amyloidosis. Recognition of this radiological pattern is important to avoid misdiagnosis and unnecessary invasive investigations.