Abdominal aortic aneurysm in a patient with situs ambiguous and polyspleny (heterotaxy syndrome): a very rare occurrence in vascular surgery! Short literature review.

PURPOSE: Situs ambiguous with polypsleny or heterotaxy syndrome is a rare occurrence in vascular surgery. METHODS: We report, for the first time in the literature, the association of situs ambiguous with polyspleny with an infrarenal aortic aneurysm. CT-scan performed to evaluate the aortic aneurysm incidentally revealed the situs ambiguous. RESULTS: CT-scan was analysed to report all anomalies of situs ambiguous in this patient. CONCLUSION: This article provides an update on the various abdominal anomalies encountered in situs ambiguous. This syndrome is poorly known in vascular surgery, particularly with regard to its surgical implications.