Intrasellar symptomatic salivary gland choristoma: a case report and literature review.

BACKGROUND: Symptomatic ectopic salivary tissue in the sellar region is extremely rare. A few cases were reported in the literature. Its radiological features overlap with those of other sellar lesions, making a definitive preoperative diagnosis difficult. This case report presents the youngest treated symptomatic patient who was diagnosed with ectopic salivary tissue in the sellar region. CASE DESCRIPTION: A 6-year-old symptomatic girl presented with chronic headache, polyuria, polydipsia, and short stature. The hormonal assay revealed hypopituitarism with low growth hormone. Magnetic resonance imaging (MRI) of the brain demonstrated a cystic sellar lesion with an enhanced intracystic nodule. The cyst was drained, and the nodule was grossly resected via an endoscopic endonasal transsphenoidal approach. Histopathological examination confirmed a salivary gland choristoma. Postoperatively, she was started on hormone replacement therapy. Follow-up brain imaging showed no evidence of residual lesion. CONCLUSION: Sellar salivary choristoma is extremely rare in pediatric population. Histopathology examination is crucial for diagnosis. Surgical treatment of a symptomatic case has a favorable prognosis.